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A Woman in Her 40s With Transient Neurological Symptoms, Migraine Headaches, and Hearing Loss

Educational Objective
Based on this clinical scenario and the accompanying image, understand how to arrive at a correct diagnosis.
1 Credit CME

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Article Information

Corresponding Author: David A. Roshal, DO, Jefferson Health, 435 Hurffville Cross-Keys Rd, Washington Township, NJ 08012 (david.roshal@jefferson.edu).

Published Online: March 11, 2019. doi:10.1001/jamaneurol.2019.0186

Conflict of Interest Disclosures: None reported.

Additional Contributions: We thank the patient for granting permission to publish this information.

References
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Rennebohm  R, Daroff  RB.  In memoriam: John O. Susac, MD (1940–2012).  Neurology. 2012;79(3):211-212. doi:10.1212/WNL.0b013e31825fe142PubMedGoogle ScholarCrossref
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Rennebohm  R, Susac  JO, Egan  RA, Daroff  RB.  Susac’s Syndrome—update.  J Neurol Sci. 2010;299(1-2):86-91. doi:10.1016/j.jns.2010.08.032PubMedGoogle ScholarCrossref
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O’Halloran  HS, Pearson  PA, Lee  WB, Susac  JO, Berger  JR.  Microangiopathy of the brain, retina, and cochlea (Susac syndrome): a report of five cases and a review of the literature.  Ophthalmology. 1998;105(6):1038-1044. doi:10.1016/S0161-6420(98)96005-5PubMedGoogle ScholarCrossref
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Susac  JO.  Susac’s syndrome: the triad of microangiopathy of the brain and retina with hearing loss in young women.  Neurology. 1994;44(4):591-593. doi:10.1212/WNL.44.4.591PubMedGoogle ScholarCrossref
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Rennebohm  RM, Egan  RA, Susac  JO.  Treatment of Susac’s syndrome.  Curr Treat Options Neurol. 2008;10(1):67-74. doi:10.1007/s11940-008-0008-yPubMedGoogle ScholarCrossref
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Vishnevskia-Dai  V, Chapman  J, Sheinfeld  R,  et al.  Susac syndrome: clinical characteristics, clinical classification, and long-term prognosis.  Medicine (Baltimore). 2016;95(43):e5223. doi:10.1097/MD.0000000000005223PubMedGoogle ScholarCrossref
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Nazari  F, Azimi  A, Abdi  S.  What is Susac syndrome? a brief review of articles.  Iran J Neurol. 2014;13(4):209-214.PubMedGoogle Scholar
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Thompson  AJ, Banwell  BL, Barkhof  F,  et al.  Diagnosis of multiple sclerosis: 2017 revisions of the McDonald criteria.  Lancet Neurol. 2018;17(2):162-173. doi:10.1016/S1474-4422(17)30470-2PubMedGoogle ScholarCrossref
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Davatchi  F.  Diagnosis/classification criteria for Behcet’s disease.  Patholog Res Int. 2012;2012:607921.PubMedGoogle Scholar
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