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Unilateral Leg Swelling in a Young Woman

Educational Objective
Based on this clinical scenario and the accompanying image, understand how to arrive at a correct diagnosis.
1 Credit CME

A 33-year-old woman with a history of hereditary bilateral retinoblastoma as an infant presented to a primary care clinic with 1 week of right lower extremity swelling. At age 8 months, she was treated with right enucleation and left eye radiotherapy (50.4 Gy). At age 4 years, she developed a recurrence of the retinoblastoma in the nasal cavity and was treated with 4 cycles of vincristine, doxorubicin, and cyclophosphamide followed by 1 cycle of cisplatin, etoposide, and intrathecal cytarabine.

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A 33-year-old woman with a history of hereditary bilateral retinoblastoma as an infant presented to a primary care clinic with 1 week of right lower extremity swelling. At age 8 months, she was treated with right enucleation and left eye radiotherapy (50.4 Gy). At age 4 years, she developed a recurrence of the retinoblastoma in the nasal cavity and was treated with 4 cycles of vincristine, doxorubicin, and cyclophosphamide followed by 1 cycle of cisplatin, etoposide, and intrathecal cytarabine.

Primary care evaluation was prompted by her mother, as the patient had not noticed her lower extremity edema. She had no fevers, weight loss, shortness of breath, chest pain, abdominal pain, or history of deep vein thrombosis. Her physical examination was notable for firm, nonpitting edema to the hip. She did not have any associated tenderness, inguinal lymphadenopathy, or palpable abdominal masses. Her vital signs were within normal limits and she ambulated comfortably. Laboratory work results, including a complete blood cell count with a differential, comprehensive metabolic panel, and D-dimer levels, were within normal limits. Doppler ultrasonography of her right lower extremity showed no deep vein thrombosis. A computed tomography venogram demonstrated a 4.0 × 3.5 cm mass of likely vascular origin that was extending into the right common iliac vein (Figure).

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Article Information

Corresponding Author: Jason Lambden, MSPH, MD, Department of Internal Medicine, McGaw Medical Center of Northwestern University, 251 E Huron St, Chicago, IL 60611 (jason.lambden@northwestern.edu).

Published Online: September 2, 2021. doi:10.1001/jamaoncol.2021.3811

Conflict of Interest Disclosures: None reported.

Additional Contributions: We thank the patient for granting permission to publish this information and Seth Pollack, MD, Northwestern Medicine, for his contributions, for which he was not compensated.

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AMA CME Accreditation Information

Credit Designation Statement: The American Medical Association designates this Journal-based CME activity activity for a maximum of 1.00  AMA PRA Category 1 Credit(s)™. Physicians should claim only the credit commensurate with the extent of their participation in the activity.

Successful completion of this CME activity, which includes participation in the evaluation component, enables the participant to earn up to:

  • 1.00 Medical Knowledge MOC points in the American Board of Internal Medicine's (ABIM) Maintenance of Certification (MOC) program;;
  • 1.00 Self-Assessment points in the American Board of Otolaryngology – Head and Neck Surgery’s (ABOHNS) Continuing Certification program;
  • 1.00 MOC points in the American Board of Pediatrics’ (ABP) Maintenance of Certification (MOC) program;
  • 1.00 Lifelong Learning points in the American Board of Pathology’s (ABPath) Continuing Certification program; and
  • 1.00 credit toward the CME of the American Board of Surgery’s Continuous Certification program

It is the CME activity provider's responsibility to submit participant completion information to ACCME for the purpose of granting MOC credit.

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