[Skip to Content]
[Skip to Content Landing]

Unusually Unnerved

Educational Objective
Based on this clinical scenario and the accompanying image, understand how to arrive at a correct diagnosis.
1 Credit CME

A 47-year-old woman was seen with left-sided facial weakness and swelling for 2 months. She was diagnosed as having recurrent high-grade serous cystadenocarcinoma of the ovary and developed these symptoms after cycle 4 of chemotherapy. She was receiving oral antidiabetic agents, and her blood glucose level was 110 mg/dL (to convert to millimoles per liter, multiply by 0.0555). Physical examination findings were consistent with left lower-motor-neuron type of facial nerve palsy. She was conscious and well oriented, with no other relevant clinical signs or focal neurological deficits. There was no history of prior COVID-19 infection. Magnetic resonance imaging (MRI) of the brain was requested, with clinical suspicion of metastasis in view of mildly elevated CA125 levels.

Please finish quiz first before checking answer.

You answered correctly!

Read the answer below and download your certificate.

You answered incorrectly.

Read the discussion below and retake the quiz.

C. Invasive fungal sinusitis (mucormycosis) with perineural spread

Overall, imaging features are highly suggestive of invasive fungal sinusitis with distinctive perineural spread of infection along the facial nerve and occult spread to the mandibular nerve via their intraparotid intercommunication. The patient started taking antifungal therapy (liposomal amphotericin B), and a biopsy was performed from the cheek lesion that yielded granulomatous inflammation. The strong clinicoradiological suspicion of fungal disease prompted a functional endoscopic sinus surgery exploration, which revealed cheesy, purulent discharge in both maxillary sinuses. The posterior wall of maxillary sinus, which was destroyed and sequestrum-like, was sampled. Histopathological examination with a fluorescent stain (Calcofluor White Stain) and Gomori methenamine silver stain (as shown in Figure 2) revealed aseptate fungal hyphae, highly suggestive of mucormycosis. Automated culture reports showed good sensitivity to voriconazole, to which the patient showed good clinical response. Although perineural spread is classically encountered with head and neck malignant tumors, the diffuse maxillary sinusitis bilaterally without any mass in the presence of a history of cancer chemotherapy strongly suggests an infectious cause.

Survey Complete!

Sign in to take quiz and track your certificates

Buy This Activity
Our websites may be periodically unavailable between 7:00pm CT June 10, 2023 and 1:00am CT June 11, 2023 for regularly scheduled maintenance.

JN Learning™ is the home for CME and MOC from the JAMA Network. Search by specialty or US state and earn AMA PRA Category 1 Credit(s)™ from articles, audio, Clinical Challenges and more. Learn more about CME/MOC

CME Disclosure Statement: Unless noted, all individuals in control of content reported no relevant financial relationships. If applicable, all relevant financial relationships have been mitigated.

Article Information

Corresponding Author: Vasundhara Patil, MBBS, MD, Tata Memorial Hospital, Mumbai and Homi Bhabha Institute, Ernest Borges Marg, Mumbai 400022, India (vsmriti@yahoo.com).

Published Online: May 18, 2023. doi:10.1001/jamaoto.2023.0802

Conflict of Interest Disclosures: None reported.

Additional Contributions: We thank the patient for granting permission to publish this information.

References
1.
Pal  R , Singh  B , Bhadada  SK ,  et al.  COVID-19–associated mucormycosis: an updated systematic review of literature.   Mycoses. 2021;64(12):1452-1459. doi:10.1111/myc.13338 PubMedGoogle ScholarCrossref
2.
Lersy  F , Royer-Leblond  J , Lhermitte  B ,  et al.  Cerebral mucormycosis: neuroimaging findings and histopathological correlation.   J Neurol. 2022;269(3):1386-1395. doi:10.1007/s00415-021-10701-8 PubMedGoogle ScholarCrossref
3.
Frater  JL , Hall  GS , Procop  GW .  Histologic features of zygomycosis: emphasis on perineural invasion and fungal morphology.   Arch Pathol Lab Med. 2001;125(3):375-378. doi:10.5858/2001-125-0375-HFOZ PubMedGoogle ScholarCrossref
4.
Margo  CE , Linden  C , Strickland-Marmol  LB , Denietolis  AL , McCaffrey  JC , Kirk  N .  Rhinocerebral mucormycosis with perineural spread.   Ophthalmic Plast Reconstr Surg. 2007;23(4):326-327. doi:10.1097/IOP.0b013e318070855b PubMedGoogle ScholarCrossref
5.
Kondapavuluri  SK , Anchala  VKR , Bandlapalli  S ,  et al.  Spectrum of MR imaging findings of sinonasal mucormycosis in post COVID-19 patients.   Br J Radiol. 2021;94(1127):20210648. doi:10.1259/bjr.20210648PubMedGoogle ScholarCrossref
6.
McLean  FM , Ginsberg  LE , Stanton  CA .  Perineural spread of rhinocerebral mucormycosis.   AJNR Am J Neuroradiol. 1996;17(1):114-116.PubMedGoogle Scholar
AMA CME Accreditation Information

Credit Designation Statement: The American Medical Association designates this Journal-based CME activity activity for a maximum of 1.00  AMA PRA Category 1 Credit(s)™. Physicians should claim only the credit commensurate with the extent of their participation in the activity.

Successful completion of this CME activity, which includes participation in the evaluation component, enables the participant to earn up to:

  • 1.00 Medical Knowledge MOC points in the American Board of Internal Medicine's (ABIM) Maintenance of Certification (MOC) program;;
  • 1.00 Self-Assessment points in the American Board of Otolaryngology – Head and Neck Surgery’s (ABOHNS) Continuing Certification program;
  • 1.00 MOC points in the American Board of Pediatrics’ (ABP) Maintenance of Certification (MOC) program;
  • 1.00 Lifelong Learning points in the American Board of Pathology’s (ABPath) Continuing Certification program; and
  • 1.00 credit toward the CME [and Self-Assessment requirements] of the American Board of Surgery’s Continuous Certification program

It is the CME activity provider's responsibility to submit participant completion information to ACCME for the purpose of granting MOC credit.

Close
Want full access to the AMA Ed Hub?
After you sign up for AMA Membership, make sure you sign in or create a Physician account with the AMA in order to access all learning activities on the AMA Ed Hub
Buy this activity
Close
Want full access to the AMA Ed Hub?
After you sign up for AMA Membership, make sure you sign in or create a Physician account with the AMA in order to access all learning activities on the AMA Ed Hub
Buy this activity
Close
With a personal account, you can:
  • Access free activities and track your credits
  • Personalize content alerts
  • Customize your interests
  • Fully personalize your learning experience
Education Center Collection Sign In Modal Right
Close

Name Your Search

Save Search
With a personal account, you can:
  • Access free activities and track your credits
  • Personalize content alerts
  • Customize your interests
  • Fully personalize your learning experience
Close
Close

Lookup An Activity

or

My Saved Searches

You currently have no searches saved.

Close

My Saved Courses

You currently have no courses saved.

Close